PubMed journal article [Idiopathic pulmonary hemosiderosis were found in PRIME PubMed. Download Source. Revista chilena de pediatrĂ­a pg PubMed journal article [Idiopathic pulmonary hemosiderosis: review of literature and case report were found in La Pediatria Sep 30 pg Revista Cubana de PediatrĂ­a Idiopathic pulmonary hemosiderosis is those processes characterized by anomalous depots of hemosiderin in the pulmonary.

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After ppediatria days, he maintained fever and the chest radiograph showed a diffuse bilateral opacity with ill-defined edges, interpreted as an atypical pneumonia, and he was started on clarithromycin. Diffuse bilateral opacity with ill-defined edges, with a predominantly central location. There are several known causes of diffuse alveolar hemorrhage vasculitides, connective tissue disorders, Heiner’s syndrome, cardiovascular diseases, among others.

Fax 55 21 E-mail: A favorable prognosis may be expected in pdiatria case, as there were no major episodes of hemorrhage and response to therapy was favorable. How to cite this article. As an outpatient, he received weekly intravenous iron therapy and investigation of anemia was continued.

Severe iron-deficiency anemia as initial manifestation of pulmonary hemosiderosis in a child

After starting steroid treatment there was a progressive increase in Hb level and improvement of radiological abnormalities. Eur J Med Res. Subsequently, there was laboratory improvement and corticosteroid was tapered.

Contudo, o acompanhamento da paciente por quatro anos afastou estas possibilidades, bem como a possibilidade de colagenoses e vasculites. The prognosis of idiopathic PH tends to improve with age and is more favorable when the diagnosis is made before the progression to pulmonary fibrosis.


The chest radiograph showed a diffuse bilateral opacity with ill-defined edges, with a predominantly central location Figure 1suggestive of alveolar hemorrhage. Idiopathic pulmonary hemosiderosis is a potentially fatal disease that results from episodes of alveolar hemorrhage of unknown origin.

Analytically he had Hb of 2. After the etiological study, the diagnosis of idiopathic pulmonary hemosiderosis was made by exclusion. For this reason, he was not submitted to an upper esophagogastroduodenoscospy, as previously planned.

Chloroquine in idiopathic pulmonary hemosiderosis. Treatment of idiopathic pulmonary hemosiderosis with inhaled flunisolide. Long-term outcome of idiopathic pulmonary hemosiderosis in children. CiteScore measures average citations received per document published. He had no macroscopic blood loss, either from gastrointestinal or urinary tract. The Spanish Association of Pediatrics has as one of its main objectives the dissemination of rigorous and updated scientific information on the different areas of pediatrics.

The clinical suspicion of alveolar hemorrhage was raised by the lack of response to iron therapy, with a progressive decrease in Hb levels and after extensive investigation of other potential sources of bleeding. Vitamin B 12 and folic acid were within normal range and the bone marrow smear was compatible with sideropenia. He was pale, prostrated and tachypneic, with dispersed bilateral rhonchi on pulmonary auscultation.

J Paediatr Child Health. As there was a poor response to intravenous iron therapy, he was readmitted to further investigate gastrointestinal bleeding. No dia seguinte, mantinha-se grave, com piora do hemograma Hct: Idiopathic pulmonary hemosiderosis in adults: Diffuse increase of the parenchyma’s density with no zone predominance, with dispersed hemksiderosis of lower density, and several small dispersed nodules. Si continua navegando, consideramos que acepta su uso.


The cytological exam of the bronchoalveolar lavage showed hemosiderin-laden macrophages. Hemosiderin-laden macrophages were also identified using Perls stain Figure 2confirming the diagnosis of PH.

A azatioprina foi hemosiderosls isoladamente. Idiopathic PH has been associated with celiac disease and, therefore, this condition should be excluded in these patients. After 6 days, he was discharged on oral iron therapy, with Hb of 8.

He was initiated on corticosteroid therapy, later associated to an immunosuppressive agent, with subsequent correction of anemia and of the radiological pattern. This case highlights the importance of including chest radiography in the investigation of blood loss of unknown origin. Bronchoalveolar hemosiderosiw fluid showing numerous hemosiderin-laden macrophages stained positive with Perls. National Center for Biotechnology InformationU.

Severe iron-deficiency anemia as initial manifestation of pulmonary hemosiderosis in a child

To improve our services and products, we use “cookies” own or third parties authorized to show advertising related to client preferences through the analyses of navigation customer behavior. SCS Quadra 1, Bl. J Hwmosiderosis Case Rep.